Cutaneous mastocytosis pediatric-onset
A case report
DOI:
https://doi.org/10.29176/30284163.1958Keywords:
Cutaneous mastocytosis, Bullous mastocytosis, urticaria pigmentosum.Abstract
Background: Cutaneous Mastocytosis (CM) is a rare entity in pediatrics, it is the most common clinical presentation of mastocytosis and is characterized by a variable clinical presentation, in which subtypes have been identified such as: maculopapular, bullous, nodular, diffuse cutaneous, mastocytoma, among others.
Case summary: We discuss the case of a 4-month-old patient who was admitted to the emergency department due to fever and generalized bullous lesions. An initial diagnostic approach to the febrile syndrome due to Staphylococcal Scalded Skin Syndrome (SSSS) was carried out, with the subsequent performance of a skin biopsy, which identified superficial dermal and perivascular infiltrate of predominantly mononuclear with interstitial mast cells, which was identified as cutaneous bullous mastocytosis and comprehensive management was initiated.
Conclusions: Since cutaneous mastocytosis is an uncommon entity in pediatrics, for that reason it is extremely important to obtain an early and accurate diagnosis, since late establishment of appropriate treatment could lead to the development of systemic forms that could put the patient's life at risk. Comprehensive treatment will depend on the extent of the lesions and the involvement of other systems, varying from pharmacological management to surgical procedures for debridement of necrotic tissue.
Author Biographies
Koretta Esmeral Atehortúa, Hospital Universidad del Norte, Barranquilla, Atlántico
Residente de Pediatría, Universidad del Norte. Departamento de Pediatría, Hospital Universidad del Norte, Barranquilla, Atlántico.
Bruny Llamas-Castellanos, Universidad de Cartagena, Cartagena, Bolívar
Residente de Dermatología, Universidad de Cartagena, Cartagena, Bolívar.
Julián Villa-Rosero, Universidad de Cartagena, Cartagena, Bolívar
Residente de Pediatría, Universidad de Cartagena, Cartagena, Bolívar.
Camila Pacheco-Paredes, Universidad Libre, Barranquilla, Atlántico
Residente de Pediatría, Universidad Libre, Barranquilla, Atlántico.
Mariana Carrillo-Borja, Universidad del Norte, Barranquilla, Atlántico
Estudiante de Pregrado de Medicina, Universidad del Norte, Barranquilla, Atlántico.
Valeria Londoño-Daguer, Universidad del Norte, Barranquilla, Atlántico.
Médico general, Universidad del Norte, Barranquilla, Atlántico.
Erick Álvarez Pereira, Universidad de Cartagena, Cartagena, Bolívar
Médico dermatólogo, Universidad de Cartagena, Cartagena, Bolívar.
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Copyright (c) 2024 Koretta Esmeral Atehortúa, Bruny Llamas-Castellanos, Julián Villa-Rosero, Camila Pacheco-Paredes, Mariana Carrillo-Borja, Valeria Londoño-Daguer, Erick Álvarez Pereira
This work is licensed under a Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International License.
